Bilateral Idiopathic Retinal Vasculitis, Aneurysm And Neuro-Retinitis (IRVAN): A Case Report

Abstract

A teenage girl presented with posterior uveitis with retinal vasculitis, aneurysm and neuro-retinitis and a gradual decrease in vision bilaterally. There was peripheral vascular non-perfusion the aetiology of which was not found. Optical coherence tomography (OCT) and fundus fluorescein angiography (FFA) pictures are presented. The treatment included intravitreal bevacizumab injection (IVBI), systemic steroid, cyclosporine and pan retinal photocoagulation. Subsequent prevention of relapse was achieved by mycophenolate mofetil (MMF). The vision improved to 30/20 and was stable 7 years after management. To the best of our knowledge, a case with seven years follow up has not been previously described.

References

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