Retinal detachment in Stickler syndrome: A review of surgical outcomes and prognosis

Abstract

Stickler syndrome is an inherited disorder of the collagen connective tissues with ophthalmic, orofacial, auditory, and articular manifestations. The risk of retinal detachment in Stickler syndrome is very high, and it is considered to be the most common cause of retinal detachment in children. Repair of retinal detachment in Stickler syndrome is challenging with variability in surgical and visual outcomes. Early diagnosis, close follow up and prompt intervention is necessary to prevent serious complication of retinal detachment and visual loss. Here we are reviewing the retinal detachment in Stickler syndrome, surgical outcomes and prognosis.

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